CFTR- France & CFTR-NGS catalog have retrieved 28 ISOSEMANTICS, which are displayed below:
#Exon/intron | Name (HGVS) | Legacy name | Class in CFTR-France | Report in CFTR-NGS | Report in CFTR-France | MAF (GnomAD) | Splicing prediction (SpliceAI) |
---|---|---|---|---|---|---|---|
Exon 4 | c.360G>A | A120A (492G/A) | VUS | CFTR-RD:1 | - | - | |
Exon 6 | c.627A>G | A209A (759A/G) | VUS | CF:2 | CF:3 CFTR-RD:1 Pending:2 | 2.1e-05 | AG: 0.02 (-47) AL: 0.00 (34) DG: 0.00 (33) DL: 0.00 (-10) |
Exon 8 | c.1116G>A | VUS | CFTR-RD:1 | - | - | ||
Exon 9 | c.1209G>A | E403E (1341G/A) | disease-causing | CF:2 | - | - | |
Exon 11 | c.1581A>G | E527E (1713A/G) | VUS | CF:1 CFTR-RD:1 | - | - | |
Exon 11 | c.1584G>A | E528E (1716G/A) | non disease-causing | Asymptomatic:2 CFTR-RD:1 Suspicion of CF:3 | Asymptomatic:1 CF:5 CFTR-RD:47 Fetal bowel anomalies:2 Pending:3 | 0.017193 | AG: 0.00 (0) AL: 0.01 (-36) DG: 0.00 (12) DL: 0.04 (0) |
Exon 13 | c.1731C>T | Y577Y (1863C/T) | VUS | - | - | ||
Exon 14 | c.1920T>C | F640F (2052T/C) | VUS | CF:1 Pending:1 | - | - | |
Exon 14 | c.2245C>T | L749L (2377C/T) | VUS | CFTR-RD:1 | - | - | |
Exon 14 | c.2259C>T | S753S (2391C/T) | VUS | CF:1 | - | - | |
Exon 15 | c.2559T>C | I853I (2691T/C) | VUS | CFTR-RD:1 | - | - | |
Exon 15 | c.2562T>C | T854T (2694T/C) | VUS | CFTR-RD:2 | - | - | |
Exon 15 | c.2562T>G | T854T (2694T/G) | non disease-causing | Asymptomatic:13 CF:5 CFTR-RD:12 Infertility:1 Pending (NBS):11 Suspicion of CF:24 | Asymptomatic:30 CF:235 CFTR-RD:445 Fetal bowel anomalies:4 Pending:63 | 0.429695 | AG: 0.00 (0) AL: 0.00 (10) DG: 0.00 (0) DL: 0.00 (-8) |
Exon 15 | c.2604A>G | V868V (2736G/A) | VUS | CF:2 CFTR-RD:1 | - | - | |
Exon 17 | c.2679G>T | G893G (2811G/T) | VUS | - | - | ||
Exon 17 | c.2898G>A | T966T (3030G/A) | non disease-causing | Suspicion of CF:1 | Asymptomatic:1 CF:3 CFTR-RD:8 Fetal bowel anomalies:2 Pending:1 | 0.008893 | AG: 0.00 (11) AL: 0.00 (-22) DG: 0.00 (6) DL: 0.01 (10) |
Exon 18 | c.2988G>A | Q996Q (3120G/A) | disease-causing | CF:2 | - | - | |
Exon 20 | c.3285A>T | T1095T (3417A/T) | VUS | Asymptomatic:1 CF:3 CFTR-RD:4 Pending:1 | - | - | |
Exon 20 | c.3288G>A | VUS | CFTR-RD:1 | - | - | ||
Exon 21 | c.3468G>A | L1156L (3600G/A) | disease-causing | CF:3 CFTR-RD:2 | - | - | |
Exon 22 | c.3681A>G | L1227L (3813A/G) | VUS | CFTR-RD:1 | - | - | |
Exon 23 | c.3837G>A | L1279L (3969G/A) | VUS | - | - | ||
Exon 23 | c.3870A>G | P1290P (4002A/G) | non disease-causing | Asymptomatic:2 CFTR-RD:2 Suspicion of CF:1 | Asymptomatic:2 CF:14 CFTR-RD:31 Pending:1 | 0.07428 | AG: 0.00 (3) AL: 0.00 (-26) DG: 0.00 (32) DL: 0.02 (3) |
Exon 24 | c.3897A>G | T1299T (4029A/G) | non disease-causing | Asymptomatic:1 CF:6 CFTR-RD:5 | - | - | |
Exon 26 | c.4188A>G | T1396T (4320A/G) | VUS | CF:1 | - | - | |
Exon 26 | c.4224G>A | 4356G/A | VUS | CF:1 | - | - | |
Exon 27 | c.4272C>T | Y1424Y (4404C/T) | non disease-causing | Suspicion of CF:2 | Asymptomatic:1 CF:9 CFTR-RD:8 | 0.006527 | AG: 0.02 (-22) AL: 0.00 (-29) DG: 0.00 (-12) DL: 0.00 (-4) |
Exon 27 | c.4389G>A | Q1463Q (4521G/A) | non disease-causing | Asymptomatic:11 CF:8 CFTR-RD:9 Infertility:1 Pending (NBS):10 Suspicion of CF:17 | Asymptomatic:27 CF:127 CFTR-RD:308 Pending:43 | 0.234066 | AG: 0.00 (17) AL: 0.00 (1) DG: 0.00 (-23) DL: 0.00 (33) |